Publication in refereed journal
香港中文大学研究人员 ( 现职)
| 孙德生教授 (医学院) |
全文
| 数位物件识别号 (DOI) http://dx.doi.org/10.1016/0167-5273(96)02713-1 |
引用次数
Web of Sciencehttp://aims.cuhk.edu.hk/converis/portal/Publication/6WOS source URL
其它资讯
摘要Hypertrophic cardiomyopathy, with myocardial fibre disarray, may occur in 20-25% of cases with Noonan's syndrome. However, dilated cardiomyopathy has not previously been reported. We describe a patient with Noonan's syndrome who presented with typical features of dilated cardiomyopathy with biventricular enlargement and left ventricular ejection fraction of 0.1http://aims.cuhk.edu.hk/converis/portal/Publication/6. Endomyocardial biopsy showed focal interstitial fibrosis and fibre hypertrophy but no disarray. This is the first report in the world literature of an association between Noonan's syndrome and dilated cardiomyopathy. It is possible that this linkage with dilated rather than hypertrophic cardiomyopathy is more common in the Chinese.
着者Yu CM, Chow LTC, Sanderson JE
期刊名称International Journal of Cardiology
出版年份199http://aims.cuhk.edu.hk/converis/portal/Publication/6
月份9
日期1
卷号5http://aims.cuhk.edu.hk/converis/portal/Publication/6
期次1
出版社ELSEVIER SCI IRELAND LTD
页次83 - 85
国际标準期刊号01http://aims.cuhk.edu.hk/converis/portal/Publication/67-5273
电子国际标準期刊号1874-1754
语言英式英语
关键词dilated cardiomyopathy; Noonan's syndrome
Web of Science 学科类别Cardiac & Cardiovascular Systems; CARDIAC & CARDIOVASCULAR SYSTEMS; Cardiovascular System & Cardiology
